Acquired hepatolenticular degeneration: is the T1 hyperintensity due to manganese deposition?
نویسندگان
چکیده
منابع مشابه
Incontinentia pigmenti with sensorimotor polyneuropathy: a novel association.
T1 relaxation time sufficient to produce pallidal T1 hyperintensity in hepatolenticular degeneration. [4] Manganese is also used as MR contrast due to the above properties but surprisingly SWI failed to show any blooming. Interestingly, calcification containing diamagnetic calcium is visualized in SWI and hence is used in the seizure MR imaging protocol.[5] The magnetic susceptibility of parama...
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Acquired hepatocerebral degeneration is a rare, mostly irreversible neurological syndrome that occurs in patients with chronic liver disease, particularly in those with surgically or spontaneously induced portosystemic shunts. Typical magnetic resonance findings are T1 hyperintensity in the pallidum, substantia nigra, periaquaductal gray matter. In this paper, we report a case of a 51-year-old ...
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INTRODUCTION AND OBJECTIVE Acquired chronic hepatocerebral degeneration, acquired hepatolenticular degeneration or pseudo-Wilson is an infrequent disorder with a hepatic origin. Cases in the literature are scarce and it is frequently confused with hepatic encephalopathy and Wilson s disease. The aim of this essay is to report a patient suffering from this disorder due to cirrhosis from non-alco...
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عنوان ژورنال:
- Neurology India
دوره 57 6 شماره
صفحات -
تاریخ انتشار 2009